Unusual case of Diastematomylia

HISTORY

• 4 year old male child-Tuft of hair over lumber spine since birth
• Born at full term §
• Pre and post-natal histories were not contributory
• Physical and mental development were normal

EXAMINATIONS

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• No neurological deficits
  • §
• Tuft of hair on the back at lumber spine
  • §
• 3D CT reconstruction
  • §
• MRI lumbosacaral spine

INTRA-OPERATIVE FINDINGS

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• Hypertrophic posterior elements §
• Two bony spurs at L1 and L3, covered by dural sleeves, extradural in location
• Type 1 SCM
• The two spurs were complete i.e. from vertebral body to lamina
• Upper spur was cephalad and the lower one was caudal in direction
• Postoperative period uneventful

TREATMENT

§D12-L4 laminectomy with excision of bony spurs L1 and L3 with detethering of cord done on 17.03.11

37 year female who is suffering from Episodic headache

Episodic headache with blurring of vision and giddiness- 4 months

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Sudden onset of severe headache followed by brief loss of consciousness on 20.11.2009.

n

Headache lasted 4 days, recovery complete

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NCCT head –Normal